Hepatic porphyrias are genetic disorders caused by the defect in an enzyme involved in heme synthesis and accumulation of heme precursors. Hepatic porphyrias include acute intermittent porphyria, variegate porphyria, aminolevulinic acid dehydratase deficiency porphyria, hereditary coproporphyria, and porphyria cutanea tarda. The acute hepatic porphyrias are manifest as neurological attacks (seizures, psychosis, severe abdominal and back pain, and acute polyneuropathy) and, to a lesser extent, with cutaneous manifestations such as photosensitive blistering rash or hypertrichosis. This activity reviews the pathophysiology, evaluation, and management of acute hepatic porphyrias and highlights the role of the interprofessional team in caring for patients affected by these conditions.
- Provider:StatPearls, LLC
- Activity Link: https://www.statpearls.com/ArticleLibrary/viewarticle/42766
- Start Date: 2023-09-01 05:00:00
- End Date: 2023-09-01 05:00:00
- Credit Details: IPCE Credits: 1.0 hours
AMA PRA Category 1 Credit™️: 1.0 hours
Nursing: 1.0 hours
Pharmacy: 1.0 hours - MOC Credit Details: ABS - 1.0 Point; Credit Type(s): Accredited CME (ABS)
ABPATH - 1.0 Point; Credit Type(s): Lifelong Learning (ABPATH)
ABA - 1.0 Point; Credit Type(s): Lifelong Learning (ABA)
ABIM - 1.0 Point; Credit Type(s): Medical Knowledge (ABIM)
ABS - 1.0 Point; Credit Type(s): Self-Assessment (ABS)
ABP - 1.0 Point; Credit Type(s): Lifelong Learning and Self-Assessment (ABP) - Commercial Support: No
- Activity Type: Enduring Material
- CME Finder Type: Online Learning
- Fee to Participate: Variable
- Measured Outcome: Learner Knowledge, Learner/Team Competence
- Provider Ship: Directly Provided
- Registration: Open to all
- Specialty: Adolescent Medicine, Cardiovascular Disease, Clinical Pathology, Critical Care Medicine, Cytopathology, Dermatopathology, Endocrinology, Diabetes, and Metabolism, Forensic Pathology, Gastroenterology, General Pediatrics, General Surgery, GI (incl. Liver, Pancreas, Bilary), Hematology, Hematology (Blood, BM), Hospital Medicine, Infectious Disease, Internal Medicine, Medical Oncology, Neurocritical Care, Pain Medicine, Pediatric Critical Care Medicine, Pediatric Emergency Medicine, Pediatric Gastroenterology, Pediatric Hematology-Oncology, Pediatric Neurology, Pulmonary Disease, Surgical Critical Care, Transplant Hepatology