Ebstein Anomaly and Malformation

Ebstein Anomaly and Malformation

Ebstein anomaly is a rare congenital heart disease characterized by apical displacement of the tricuspid valve, adherence of the septal and posterior leaflets to the myocardium, and atrialization of the inlet portion of the right ventricle. This malformation is usually accompanied by tricuspid regurgitation, right ventricular failure, and arrhythmias. While most patients with Ebstein anomaly will be symptomatic at birth or in early childhood, some patients will not be diagnosed until their sixth or seventh decade. The clinical manifestations of Ebstein anomaly range from asymptomatic to severe as dictated by the degree of tricuspid valve displacement, severity of tricuspid regurgitation, effective right ventricular volume, and the presence of associated malformations such as an atrial septal defect or pulmonary valve stenosis or atresia. Arrhythmias are common and protracted in patients with Ebstein anomaly due to accessory pathways and right atrial dilatation. The common presenting symptoms of this cardiac malformation include cyanosis, heart failure, and tachyarrhythmias; exertional dyspnea is common in older patients with Ebstein anomaly. Surgical intervention with or without catheter-directed ablation is commonly required.This activity for healthcare professionals reviews the etiology, epidemiology, pathophysiologic mechanisms, clinical presentation, evaluation, and management of Ebstein anomaly and highlights the role of the interprofessional team in improving outcomes for patients with this rare but complex cardiac malformation.

  • Provider:StatPearls, LLC
  • Activity Link: https://www.statpearls.com/ArticleLibrary/viewarticle/20850
  • Start Date: 2023-09-01 05:00:00
  • End Date: 2023-09-01 05:00:00
  • Credit Details: AMA PRA Category 1 Credit™️: 2.0 hours
    Nursing: 2.0 hours
    Pharmacy: 2.0 hours
  • MOC Credit Details: ABS - 2.0 Point; Credit Type(s): Accredited CME (ABS)
    ABPATH - 2.0 Point; Credit Type(s): Lifelong Learning (ABPATH)
    ABA - 2.0 Point; Credit Type(s): Lifelong Learning (ABA)
    ABTS - 2.0 Point; Credit Type(s): Accredited CME (ABTS)
    ABIM - 2.0 Point; Credit Type(s): Medical Knowledge (ABIM)
    ABS - 2.0 Point; Credit Type(s): Self-Assessment (ABS)
    ABP - 2.0 Point; Credit Type(s): Lifelong Learning and Self-Assessment (ABP)
    ABTS - 2.0 Point; Credit Type(s): Self-Assessment (ABTS)
  • Commercial Support: No
  • Activity Type: Enduring Material
  • CME Finder Type: Online Learning
  • Fee to Participate: Variable
  • Measured Outcome: Learner Knowledge, Learner/Team Competence
  • Provider Ship: Directly Provided
  • Registration: Open to all
  • Specialty: Adolescent Medicine, Adult Congenital Heart Disease, Advanced Heart Failure and Transplant Cardiology, Cardiac Anesthesia, Cardiovascular, Cardiovascular Disease, Congenital Cardiac, General Pediatrics, General Surgery, Hospital Medicine, Internal Medicine, Molecular Genetic Pathology, Neonatal-Perinatal Medicine, Pediatric Cardiology, Pediatric Critical Care Medicine, Pediatric Emergency Medicine, Pediatric Pathology, Pediatric Surgery
«
Subscribe
Notify of
guest
0 Comments
Oldest
Newest Most Voted
Inline Feedbacks
View all comments
0
Would love your thoughts, please comment.x
()
x

Contact us

If you want to join leaders who will shape what Americans think about sleep.

Name(Required)
Sign Up
This field is for validation purposes and should be left unchanged.

Sign up for the expert list

for media inquiries

Name(Required)
Sign Up
This field is for validation purposes and should be left unchanged.