Idiopathic pulmonary fibrosis (IPF) is a progressive lung disorder characterized by scarring of the lungs from an unknown cause. The condition has a poor long-term prognosis. Classic features of IPF include the gradual onset of shortness of breath, progressive dyspnea, and a dry, nonproductive cough. Pulmonary function tests usually reveal restrictive lung function impairment, decreased functional vital capacity, and diminished carbon monoxide diffusing capacity. Early diagnosis is pivotal for effective management, given the disease’s tendency to progress rapidly in advanced stages. Diagnosis can often be established without biopsy through a comprehensive assessment of clinical history, imaging results, and exclusion of alternative conditions. However, a lung biopsy may be required in cases where diagnostic uncertainty persists.Imaging techniques, particularly computed tomography scans, frequently display a distinctive pattern of fibrosis, typically observed at the periphery of both lungs and more prominently concentrated at the bases, aiding in the diagnosis of IPF. In cases of diagnostic uncertainty, a lung biopsy can confirm the diagnosis. Treatment strategies include supportive measures, oxygen supplementation as required, antifibrotic medications, and, in severe cases, lung transplantation, which stands as the sole curative option. This activity comprehensively reviews the etiology, epidemiology, clinical manifestations, evaluation, and management of IPF in adults, highlighting the role of the interprofessional healthcare team in its evaluation, diagnosis, and management.
- Provider:StatPearls, LLC
- Activity Link: https://www.statpearls.com/ArticleLibrary/viewarticle/28027
- Start Date: 2023-09-01 05:00:00
- End Date: 2023-09-01 05:00:00
- Credit Details: IPCE Credits: 1.5 hours
AMA PRA Category 1 Credit™️: 1.5 hours
Nursing: 1.5 hours
Pharmacy: 1.5 hours - MOC Credit Details: ABS - 1.5 Point; Credit Type(s): Accredited CME (ABS)
ABPATH - 1.5 Point; Credit Type(s): Lifelong Learning (ABPATH)
ABA - 1.5 Point; Credit Type(s): Lifelong Learning (ABA)
ABTS - 1.5 Point; Credit Type(s): Accredited CME (ABTS)
ABIM - 1.5 Point; Credit Type(s): Medical Knowledge (ABIM)
ABS - 1.5 Point; Credit Type(s): Self-Assessment (ABS)
ABTS - 1.5 Point; Credit Type(s): Self-Assessment (ABTS) - Commercial Support: No
- Activity Type: Enduring Material
- CME Finder Type: Online Learning
- Fee to Participate: Variable
- Measured Outcome: Learner Knowledge, Learner/Team Competence
- Provider Ship: Directly Provided
- Registration: Open to all
- Specialty: Ambulatory/Outpatient, Cardiac Anesthesia, Cardiothoracic, Critical Care Medicine, General Operative Anesthesia, General Thoracic, Geriatric Medicine, Hospice and Palliative Medicine, Hospital Medicine, Internal Medicine, Pulmonary Disease, Pulmonary, Mediastinum, Rheumatology, Sleep Medicine, Surgical Critical Care, Thoracic Anesthesia