Pantothenate kinase-associated neurodegeneration (PKAN), formerly known as Hallervorden-Spatz disease, is a rare autosomal recessive neurodegenerative disorder associated with iron accumulation in the brain nuclei and characterized by progressive extrapyramidal dysfunction and dementia. Classically, the disease presents between ages 7 and 15 years. However, the disease onset has been reported in all age groups, including infancy and adulthood. As PKAN has an autosomal mode of inheritance, each sibling of an individual has a 25% chance of being affected and a 50% chance of being an asymptomatic carrier. This activity reviews the evaluation and management of pantothenate kinase-associated neurodegeneration and highlights the role of the interprofessional team in the care of affected patients and their families.
- Provider:StatPearls, LLC
- Activity Link: https://www.statpearls.com/ArticleLibrary/viewarticle/22494
- Start Date: 2023-09-01 05:00:00
- End Date: 2023-09-01 05:00:00
- Credit Details: AMA PRA Category 1 Credit™️: 1.0 hours
Nursing: 1.0 hours
Pharmacy: 1.0 hours - MOC Credit Details: ABS - 1.0 Point; Credit Type(s): Accredited CME (ABS)
ABPATH - 1.0 Point; Credit Type(s): Lifelong Learning (ABPATH)
ABA - 1.0 Point; Credit Type(s): Lifelong Learning (ABA)
ABIM - 1.0 Point; Credit Type(s): Medical Knowledge (ABIM)
ABS - 1.0 Point; Credit Type(s): Self-Assessment (ABS)
ABP - 1.0 Point; Credit Type(s): Lifelong Learning and Self-Assessment (ABP) - Commercial Support: No
- Activity Type: Enduring Material
- CME Finder Type: Online Learning
- Fee to Participate: Variable
- Measured Outcome: Learner Knowledge, Learner/Team Competence
- Provider Ship: Directly Provided
- Registration: Open to all
- Specialty: Adolescent Medicine, Developmental-Behavioral Pediatrics, General Pediatrics, General Surgery, Hospice & Palliative Medicine, Hospital Medicine, Internal Medicine, Molecular Genetic Pathology, Neonatal-Perinatal Medicine, Neurodevelopmental Disabilities, Neuropathology (incl. Neuromuscular), Pediatric Anesthesia, Pediatric Critical Care Medicine, Pediatric Emergency Medicine, Pediatric Neurology