Vohwinkel syndrome, also known as keratoderma hereditarian mutilans, is a rare and complex genetic disorder. This condition primarily affects the skin, resulting in palmoplantar keratoderma, characterized by thickened skin on the palms and soles. The keratoderma often forms a star-like pattern on the knuckles. Individuals with Vohwinkel Syndrome may experience pseudoainhum, a constriction of the fingers or toes, which can ultimately lead to autoamputation of the affected digits. Hearing impairment is another significant aspect of the syndrome, with cochlear involvement often requiring audiological assessment and possible cochlear implantation for management. This activity reviews the genetic basis, clinical manifestations, and treatment of Vohwinkel syndrome patients and highlights the role of the interprofessional team in improving care for affected patients.
- Provider:StatPearls, LLC
- Activity Link: https://www.statpearls.com/ArticleLibrary/viewarticle/31249
- Start Date: 2023-09-01 05:00:00
- End Date: 2023-09-01 05:00:00
- Credit Details: AMA PRA Category 1 Credit™️: 1.0 hours
Nursing: 1.0 hours
Pharmacy: 1.0 hours - MOC Credit Details: ABS - 1.0 Point; Credit Type(s): Accredited CME (ABS)
ABOS - 1.0 Point; Credit Type(s): Accredited CME (ABOS)
ABPATH - 1.0 Point; Credit Type(s): Lifelong Learning (ABPATH)
ABIM - 1.0 Point; Credit Type(s): Medical Knowledge (ABIM)
ABS - 1.0 Point; Credit Type(s): Self-Assessment (ABS)
ABP - 1.0 Point; Credit Type(s): Lifelong Learning and Self-Assessment (ABP)
ABOHNS - 1.0 Point; Credit Type(s): Self-Assessment (ABOHNS) - Commercial Support: No
- Activity Type: Enduring Material
- CME Finder Type: Online Learning
- Fee to Participate: Variable
- Measured Outcome: Learner Knowledge, Learner/Team Competence
- Provider Ship: Directly Provided
- Registration: Open to all
- Specialty: Dermatopathology, Foot and Ankle, General Pediatrics, General Surgery, Hand Surgery, Internal Medicine, Molecular Genetic Pathology, Neurotology, Pediatric Orthopaedic Surgery, Surgery of the Hand, Vascular Surgery